Albarran-Ormond syndrome
Related people
Inflammatory retroperitoneal fibrosis of unknown aetiology, which may extend into the chest cavity and pelvis, and is usually associated with urinary obstruction. Characterised by pain in the back, of variable intensity, usually progressing and radiating in pattern of urethral colic, or abdominal pain without specific localization. Pain usually persisting for a month. Frequently associated: vomiting, nausea, anorexia, malaise, fatigue, weight loss, constipation or diarrhoea, oliguria or anuria. Occurs twice as often in males as females; average age at onset 46 years for males, 32 years for females
Early casuistic descriptions by Albarran in 1905, Oberling 1925, Bachrach 1928, Putschar 1934 and Diekow 1942. The American urologist John Kelso Ormond rediscovered it in 1948. He described two patients with diffuse fibrosis of the retroperitoneal tissues, and established the clinical and pathological entity of idiopathic retroperitoneal fibrosis more clearly.
Bibliography
- J. Albarran:
Retention rénale par periurétérité. Libération externe de l’uretère.
Association française d'urologie, 1905, 9: 511. - J. K. Ormond:
Bilateral ureteral obstruction due to envelopment and compression by an inflammatory retroperitoneal process.
Journal of Urology, Baltimore, 1948, 59: 1072-1079. - J. K. Ormond:
Idiopathic retroperitoneal fibrosis: a discussion of the etiology.
Journal of Urology, Baltimore, 1965, 94: 385-390.